What Is PAH?

What is PAH, anyway?

PAH isn’t just high blood pressure. PAH is
  • The medical abbreviation (acronym) that stands for pulmonary arterial hypertension
  • A certain kind of high blood pressure in the lungs that specifically affects the way your heart and lungs work together
  • A condition that causes blood vessels in the lungs to become narrower, which means the heart must work harder to push blood through these tighter passages
High blood pressure in the lungs with magnified closeup showing narrowed blood vessels

How does PAH cause slower “traffic” in your blood vessels?

Imagine your blood vessels as the highway. Your blood cells are like the cars. When blood vessels in the lungs become narrow, it reduces the flow of blood cells—similar to the way traffic flow slows down when lanes are closed.

Traffic jam illustration

Learn how this “traffic jam” in the lungs causes changes in the heart and how treatment can help open these “closed lanes.”

PAH Effects on Heart & Lungs

Why does PAH, a lung disease, affect the heart?

When you have PAH, the blood vessels in your lungs thicken and become narrow, making your heart work harder to pump blood through them.

Click to expand transcript

PAH begins when the walls of the blood vessels in the lungs thicken and become more narrow. Because the blood vessels become more narrow, it’s harder for the blood to pass through them. The reduced blood flow that is caused by the narrowed vessels creates increased pressure on the right side of the heart. The right side of the heart tries to compensate by working harder to pump blood through the vessels and into the lungs. Over time, the heart struggles to maintain this level of intensity. It’s like asking your heart to run a marathon every minute of every day and PAH symptoms result.

How serious is PAH, and what kind of doctor should I see?

PAH is a progressive disease, meaning it gets worse over time and can eventually be fatal.

While all PAH is serious, some doctors may describe your PAH differently depending on how PAH is affecting you or how your PAH may progress. You may have heard terms like “mild,” “moderate,” or “severe” to describe how PAH affects an individual.

Learn more about how PAH specialists think about PAH severity today and what can be done about it.

PAH Life Expectancy

Patient perspective: Working with a PAH specialist

Why is it important to see a PAH specialist?

Because PAH is a serious disease that is life threatening, finding a healthcare provider who specializes in treating PAH is extremely important. Not all cardiologists and pulmonologists have expertise treating PAH. A PAH specialist has extensive training and experience in diagnosing and treating PAH, so they may be more knowledgeable about the latest treatment advances and options.

For some, finding and getting to a PAH specialist can be a challenge. You may not know where to begin your search. The Pulmonary Hypertension Association (PHA) offers a finder tool to help you get started.

Find a PAH Specialist

Learn more about PAH

Keep asking questions! The more you know about your PAH, the better equipped you will be to fight it.

Why does someone get PAH?

What Causes PAH?

What are the symptoms of PAH?

Symptoms of PAH

How is PAH diagnosed?

PAH Diagnosis & Testing