ICD-10-CM Codes for PAH

Use the following ICD-10-CM codes to classify diagnoses, symptoms, and procedures performed on patients with PAH.




Primary pulmonary hypertension


Pulmonary hypertension, unspecified


Secondary pulmonary arterial hypertension


Cor pulmonale (chronic)


Other specified pulmonary heart diseases


Pulmonary heart disease, unspecified

ICD-10-CM=International Classification of Diseases, Tenth Revision, Clinical Modification.
Reference: 1. Centers for Disease Control and Prevention. Accessed March 22, 2021. https://www.cdc.gov/nchs/icd/icd10cm_browsertool.htm
This document provides an overview of International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) diagnosis codes that have been associated with pulmonary arterial hypertension (PAH), pulmonary hypertension (PH), and interstitial lung disease (ILD). This list was developed in consultation with coding experts, providers, and third-party claims data analyses of patients with these conditions. This document is presented for informational purposes only and does not constitute reimbursement or legal advice. As third-party reimbursement is affected by many factors, United Therapeutics Corporation does not promise or guarantee coverage, levels of reimbursement, or payment.
Reimbursement policy through third-party payers is complex and updated frequently; therefore, the information presented in this document may not be current, accurate, or comprehensive. United Therapeutics Corporation strongly recommends consulting each patient’s third-party payer for the most current coding, coverage, and reimbursement policies. In no event shall United Therapeutics Corporation, UT Assist, or their employees or agents, be liable for the damages resulting from or relating to any information provided on this document.